Objective of the study. To investigate the frequency of detection and the characteristics of clinical manifestations of cystic fibrosis in children. Materials and methods. A total of 106 patients with cystic fibrosis aged from 0 months to 14 years were observed. All patients were hospitalized and treated in the departments of pulmonology, early childhood pathology, and gastroenterology. Results. In children with cystic fibrosis, the main clinical symptoms of the bronchopulmonary system were cough, dyspnea, oral rales, lethargy, and loss of appetite. Upon admission to the hospital, the general condition of most patients was assessed as severe. Conclusion. The high frequency of repeated hospitalizations and early mortality caused by severe respiratory complications indicate the need to improve programs for early detection, long-term follow-up, and multidisciplinary management of children with cystic fibrosis.

Cystic fibrosis, sweat test, children, cough

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